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Table 3 Data extraction table and summary of included studies in the present review

From: The oral phenotype and dental management in patients with maple syrup urine disease; case report and scoping review

Author

Type of study

No. of participants

Age of participant

Gender of participant

Summary of oral findings

Conclusion

Ballikaya et al., 2021 [17]

Observational

25

9.88 (range from 2 to 28)

10 females; 15 males

Plaque induced gingivitis, dental anomalies and alteration in mandibular morphology, dental caries

Impaired oral health is common among individuals with MSUD. Preventive measures and dental treatment should be included in the multidisciplinary care in MSUD.

Gazit et al., 1989 [18]

Case report

1

14

Male

Elongated and retrognathic mandible, incompetent lips, dental crowding, rampant caries, gingivitis and gingival enlargement,

Oral findings in the described patient cannot be explained solely by the biochemical or metabolic alterations in MSUD.

Fukushima et al., 1986 [20]

Case report

1

5

Female

Micrognathia, dental caries, plaque induced gingivitis

Oral findings are attributed to poor oral hygiene, abnormal eating habit, and restricted diet.

Oelgiesser et al., 2006 [23]

Case report

1

19

Female

Missing teeth due to trauma

Implant supported fixed prosthesis provides functional and esthetic solution for traumatic tooth loss in patients with MSUD.