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Table 4 Summary of information of oral findings in seven cases of Larsen syndrome presented in this study and in previous reports [15,16,17,18,19,20]

From: An orthodontic perspective on Larsen syndrome

 

Tsang et al. [15]

Chien et al. [18]

Kawahara et al. [16]

Percin et al. [19]

Kozaki et al. [20]

Sajnani et al. [17]

Present case

Age

15

29

8

14

8

8

5

Sex

Female

Female

Male

Female

Female

Male

Female

Number of abnormal teeth

11 CMT

None

4 CMT

2 CST

ND

2 CMT

2 CMT

Cleft lip and/or palate

Cleft left lip and palate

ND

Cleft palate

Cleft palate

Cleft soft palate

None

Cleft soft palate

Incisor relationship

O.J.: − 6 mm

anterior crossbite

ND

O.J.: − 2 mm

O.B.: + 5 mm

anterior crossbite

ND

Edge-to-edge bite

Anterior open bite

O.J.: + 2 mm

O.B.: + 2 mm

Posterior cross bite

Unilateral: left

Found*

Bilateral

ND

Unilateral: right

Bilateral

Unilateral: right

  1. CMT congenital missing teeth, CST congenital supernumerary teeth, O.J. overjet, O.B. overbite, ND no description
  2. *Posterior cross bite with no description as to whether unilateral or bilateral