Fig. 2From: Congenital anomalies-associated Riga–Fede disease as an early manifestation of Lesch–Nyhan syndrome: rare entities in the same pediatric patient—a case reportExtraoral examination of the patient at the age of 2.5 years. A Deformed left nasal ala and lower lip. B Evidence of a nasal ulcer with complete loss of the columella. Lip manipulation (sucking/biting) and saliva over the perioral tissues are evidentBack to article page